Morquio syndrome with acute cord compression: An anesthetic challenge

Abstract

Morquio syndrome with skeletal and extraskeletal manifestations is an anesthetic challenge. Airway management in children with Morquio syndrome can pose added risks of atlantoaxial instability, spinal cord compression, and distorted airway anatomy, leading to difficult mask ventilation and intubation. We report the anesthetic management of a 4-year-old child with Morquio syndrome who presented with acute cord compression and underwent emergency decompression of the stenotic spinal canal at the craniovertebral junction. Thorough preoperative evaluation, meticulous planning, and vigilant monitoring in the perioperative period are essential for safe anesthetic management.