Cystic Partially Differentiated Nephroblastoma, A Hyperfavourable Variant of Nephroblatoma: A Case Report with Review of the Literature

Abstract

Cystic partially differentiated nephroblastoma is a rare variant of Wilm’s tumor and it represents the hyperfavourable end of the Wilm’s spectrum affecting young children. We described the first documented case from the northern part of Nigeria. The index patient presented with left flank mass. He had unilateral nephrectomy and surgical pathology established its diagnosis. It is a lower risk but malignant tumor that comes as the differential diagnosis of pediatric cystic renal lesions and need to be differentiated from benign lesions such as cystic nephroma and mixed epithelial and stroma tumor of kidney. It should always be considered as a differential diagnosis of childhood abdominal mass with appropriate investigations and management since it is curable by nephrectomy alone.