A Huge Pleomorphic Liposarcoma of the Retroperitoneum

Abstract

common type of soft tissue sarcomas is liposarcomas. It consists of <1% of all malignant tumors in adulthood.1,2 Retroperitoneal liposarcoma (RLS), is a rare, biologically heterogeneous tumor that presents considerable challenges due to its size and deep location.1 85% of RLS are malignant tumors that remain occult for long periods and grow quite large. Their typical symptoms are discomfort, pain or a palpable mass due to large size. These tumors occur most frequently in men, generally in the fifth or sixth decade of life. Magnetic resonance imaging (MRI) provide reliable data about localization of mass and relationship between vascular structures. Although complete surgical resection is mandatory for extending survival, the majority of patients with huge RLS will develop locally recurrent disease following surgery.1-3 So that patients should be followed routinely in every 3 months during first two years .4 Pleomorphic liposarcoma is the rarest subtype and is a high grade tumor. The risk of recurrence and metastatis with liposarcoma increases with higher grade. Herein, we report a case of a 68 year-old man with a 35 cm mass adjacent to kidney with synchronous inguinal 7 cm mass.