Evaluation of clinical features and outcome of eight fetuses with ectopia cordis; A study from a fetal cardiology center

IF 1.3 4区 医学 Q3 PEDIATRICS Congenital Anomalies Pub Date : 2023-01-21 DOI:10.1111/cga.12508
Eviç Zeynep Başar, Yasemin Dogan, Özlem Kayabey, Kadir Babaoğlu
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Abstract

We aim to evaluate the clinical course and outcome of cases with a prenatal diagnosis of ectopia cordis in our center. In this retrospective study, we analyzed clinical variables including gestational age at diagnosis, maternal age, associated cardiac, extracardiac, genetic anomalies and, outcome in prenatally diagnosed ectopia cordis cases in our tertiary referral center. Eight ectopia cordis cases from seven pregnancies were included in the study. All fetuses had complete type of ectopia cordis and pentalogy of Cantrell. Five multiple pregnancies were found, four were twin pregnancies (three dichorionic diamniotic, one monochorionic monoamniotic) and one was triplet (trichorionic triamniotic). In the monochorionic monoamniotic twin pregnancy, both fetuses have pentalogy of Cantrell. Two cases had intracardiac structural defects including Tetralogy of Fallot and hypoplastic right heart syndrome. Three pregnancies were terminated, four cases delivered alive could not survive beyond the neonatal period. The striking feature in our study is its association with multiple pregnancies.

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心异位8例临床特点及预后分析一项来自胎儿心脏病中心的研究
我们的目的是评估临床过程和结果的情况下,产前诊断的心异位在我中心。在这项回顾性研究中,我们分析了临床变量,包括诊断时的胎龄、母亲年龄、相关的心脏、心外、遗传异常以及在我们三级转诊中心产前诊断的心外异位病例的预后。本研究包括7例妊娠的8例心脏异位病例。所有胎儿均有完整型心异位和Cantrell五联症。多胎妊娠5例,双胎妊娠4例(双绒毛膜双羊膜妊娠3例,单绒毛膜单羊膜妊娠1例),三胞胎妊娠1例(三绒毛膜三羊膜妊娠)。在单绒毛膜单羊膜双胎妊娠中,两个胎儿都有Cantrell五联症。2例有法洛四联症和右心发育不全综合征。3例妊娠终止,4例活产不能活过新生儿期。我们研究的显著特征是它与多胎妊娠的关联。
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来源期刊
Congenital Anomalies
Congenital Anomalies PEDIATRICS-
自引率
0.00%
发文量
49
审稿时长
>12 weeks
期刊介绍: Congenital Anomalies is the official English language journal of the Japanese Teratology Society, and publishes original articles in laboratory as well as clinical research in all areas of abnormal development and related fields, from all over the world. Although contributions by members of the teratology societies affiliated with The International Federation of Teratology Societies are given priority, contributions from non-members are welcomed.
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