A. de Lima, Stella de Souza Carneiro, Josef Murad, J. Arruda, José Guilherme Caselli, Edson Egashira
{"title":"右肺动脉缺失伴上腔静脉及肺内动脉分支高输出量冠状动脉瘘1例","authors":"A. de Lima, Stella de Souza Carneiro, Josef Murad, J. Arruda, José Guilherme Caselli, Edson Egashira","doi":"10.5935/2318-8219.20190026","DOIUrl":null,"url":null,"abstract":"Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly that occurs due to malformation of the sixth aortic arch of the affected side during embryogenesis, and may occur in isolation or in combination with other cardiovascular anomalies.1,2 Diagnosis usually occurs in adolescence, but individuals may be asymptomatic and receive late diagnosis. We report a case of symptomatic patient with right pulmonary artery agenesis accompanied by high-output fistula of the Circumflex Artery (CXA) to the Superior Vena Cava (SVC).","PeriodicalId":211175,"journal":{"name":"ARQUIVOS BRASILEIROS DE CARDIOLOGIA - IMAGEM CARDIOVASCULAR","volume":null,"pages":null},"PeriodicalIF":0.0000,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Agenesia of Right Pulmonary Artery Associated with High Output Coronary Fistula for\\n Superior Vena Cava and Intrapulmonary Artery Branches: Case Report\",\"authors\":\"A. de Lima, Stella de Souza Carneiro, Josef Murad, J. Arruda, José Guilherme Caselli, Edson Egashira\",\"doi\":\"10.5935/2318-8219.20190026\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly that occurs due to malformation of the sixth aortic arch of the affected side during embryogenesis, and may occur in isolation or in combination with other cardiovascular anomalies.1,2 Diagnosis usually occurs in adolescence, but individuals may be asymptomatic and receive late diagnosis. We report a case of symptomatic patient with right pulmonary artery agenesis accompanied by high-output fistula of the Circumflex Artery (CXA) to the Superior Vena Cava (SVC).\",\"PeriodicalId\":211175,\"journal\":{\"name\":\"ARQUIVOS BRASILEIROS DE CARDIOLOGIA - IMAGEM CARDIOVASCULAR\",\"volume\":null,\"pages\":null},\"PeriodicalIF\":0.0000,\"publicationDate\":\"1900-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"ARQUIVOS BRASILEIROS DE CARDIOLOGIA - IMAGEM CARDIOVASCULAR\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5935/2318-8219.20190026\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"ARQUIVOS BRASILEIROS DE CARDIOLOGIA - IMAGEM CARDIOVASCULAR","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5935/2318-8219.20190026","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Agenesia of Right Pulmonary Artery Associated with High Output Coronary Fistula for
Superior Vena Cava and Intrapulmonary Artery Branches: Case Report
Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly that occurs due to malformation of the sixth aortic arch of the affected side during embryogenesis, and may occur in isolation or in combination with other cardiovascular anomalies.1,2 Diagnosis usually occurs in adolescence, but individuals may be asymptomatic and receive late diagnosis. We report a case of symptomatic patient with right pulmonary artery agenesis accompanied by high-output fistula of the Circumflex Artery (CXA) to the Superior Vena Cava (SVC).