{"title":"以继发性自发性气胸为表现的Kartagener综合征:一例罕见病例报告","authors":"N. Prabhakar, R. Anand, Preetha Ramesh","doi":"10.4103/japt.japt_31_22","DOIUrl":null,"url":null,"abstract":"Kartagener's syndrome (KS) is a part of a larger family of diseases classified as primary ciliary dyskinesia (PCD). The triad of KS consists of bronchiectasis, chronic sinusitis, and situs inversus, which is likely underdiagnosed, as a limited amount of centers have resources to provide an accurate diagnosis. Symptoms are more prevalent in children that too in the first decade of life. Pneumothorax might be one of the rare complications of the PCD. A review of literature revealed that few patients are diagnosed with PCD complicated with secondary spontaneous pneumothorax. In this case report, we describe a PCD patient with spontaneous pneumothorax and how we treated him in our institution.","PeriodicalId":348236,"journal":{"name":"Journal of Association of Pulmonologist of Tamil Nadu","volume":"38 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"Kartagener's syndrome presenting with secondary spontaneous pneumothorax: A rare case report\",\"authors\":\"N. Prabhakar, R. Anand, Preetha Ramesh\",\"doi\":\"10.4103/japt.japt_31_22\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Kartagener's syndrome (KS) is a part of a larger family of diseases classified as primary ciliary dyskinesia (PCD). The triad of KS consists of bronchiectasis, chronic sinusitis, and situs inversus, which is likely underdiagnosed, as a limited amount of centers have resources to provide an accurate diagnosis. Symptoms are more prevalent in children that too in the first decade of life. Pneumothorax might be one of the rare complications of the PCD. A review of literature revealed that few patients are diagnosed with PCD complicated with secondary spontaneous pneumothorax. In this case report, we describe a PCD patient with spontaneous pneumothorax and how we treated him in our institution.\",\"PeriodicalId\":348236,\"journal\":{\"name\":\"Journal of Association of Pulmonologist of Tamil Nadu\",\"volume\":\"38 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2022-05-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of Association of Pulmonologist of Tamil Nadu\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4103/japt.japt_31_22\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of Association of Pulmonologist of Tamil Nadu","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/japt.japt_31_22","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Kartagener's syndrome presenting with secondary spontaneous pneumothorax: A rare case report
Kartagener's syndrome (KS) is a part of a larger family of diseases classified as primary ciliary dyskinesia (PCD). The triad of KS consists of bronchiectasis, chronic sinusitis, and situs inversus, which is likely underdiagnosed, as a limited amount of centers have resources to provide an accurate diagnosis. Symptoms are more prevalent in children that too in the first decade of life. Pneumothorax might be one of the rare complications of the PCD. A review of literature revealed that few patients are diagnosed with PCD complicated with secondary spontaneous pneumothorax. In this case report, we describe a PCD patient with spontaneous pneumothorax and how we treated him in our institution.