A Rare Cause of Congenital Duodenal Obstruction: Preduodenal Portal Vein

Preduodenal portal vein (PDPV) is a rare cause of duodenal obstruction. While half of PDPV cases present with obstructive findings in the neonatal period, the other half are diagnosed incidentally at advanced ages. In half of the obstructed PDPV cases, the cause of obstruction is another congenital anomaly. In our case, the aberrant ventral extension of the pancreas with PDPV caused incomplet duodenal obstruction by compressing the duodenum externally.