强直性肌营养不良的呼吸管理

Archives of Pulmonology and Respiratory Care Pub Date : 2020-05-06 DOI:10.17352/aprc.000043

J. Bach, G. Chiarello

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摘要

肌强直性营养不良患者可以通过使用连续无创通气支持(CNVS)来避免呼吸衰竭发作。在154例连续出现在神经肌肉疾病诊所的患者中，143例为1型或2型，11例为先天性肌强直性营养不良。在76名多次来过的患者中，有41人至少服用了睡眠NVS来缓解疲劳和嗜睡症状。

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Respiratory Management of Myotonic Dystrophy

Patients with myotonic dystrophy can avoid episodes of respiratory failure by using up to continuous noninvasive ventilatory support (CNVS). Of 154 patients consecutively presenting to a neuromuscular disease clinic, 143 had types 1 or 2 and 11 had congenital myotonic dystrophy. Of the 76 who came multiple times, 41 were prescribed and used at least sleep NVS to relieve symptoms of fatigue and hypersomnolence.

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Archives of Pulmonology and Respiratory Care

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