Benign paroxysmal tonic upgaze of childhood; a rare syndrome

Benign Paroxysmal Tonic Upgaze is an oculomotor syndrome which was first described by Ovurier and Billson [1]. It consists of episodes of conjugate deviation of eyes with the onset in early infancy [2]. Detailed evaluation including metabolic, electroencephalographic and neuroimaging is often normal. The exact pathogenesis is yet unknown. We report a 10 month old boy who presented with persistent tonic upgaze.