A. V. Ishbuldina, R. Rakhmaeva, A. Kamalova, D. V. Usova, A. M. Khazieva, A. M. Nigmatullina, M. S. Zainetdinova
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引用次数: 0
摘要
文章描述了一个患有 IXa 型糖原病的儿童出现肌松性肥胖的临床案例。造成肌松性肥胖的原因一方面是缺乏对患儿营养的控制:在实际饮食中摄入过多易消化的碳水化合物、脂肪和缺乏蛋白质;另一方面是由于对珀尔特氏病进行手术治疗而限制了患儿的运动量。文章以患有 IX 型糖原病、肌肉松弛性肥胖症、珀尔特氏病和嗜酸性食管炎的复杂综合征儿童为例,提供了饮食治疗处方的实用建议。
Sarcopenic obesity in a child with type IXa glycogenosis in combination with eosinophilic esophagitis and Legg–Calvé–Perthes disease
The article describes a clinical example of the development of sarcopenic obesity in a child with type IXa glycogen disease. The reasons for the development of sarcopenic obesity were, on the one hand, the lack of control over the child’s nutrition: excess consumption of easily digestible carbohydrates, fats and lack of protein in the actual diet and inactivity due to a child’s motor activity restriction in view of surgical interventions for Perthes’ disease, on the other. The article provides practical recommendations on the example of prescribing diet therapy to a child with a complex combination of type IX glycogenosis, sarcopenic obesity, Perthes disease, and eosinophilic esophagitis.