右髂腰卡波状血管内皮瘤:病例报告

IF 0.5 Q4 PEDIATRICS Egyptian Pediatric Association Gazette Pub Date : 2024-04-30 DOI:10.1186/s43054-024-00272-4
Neng Ren, Ye Gu, Na Song, Wen Qian, Wenhui Gao, Yunfeng Zhang
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引用次数: 0

摘要

卡波西瘤(Kaposiform hemangioendothelioma,KHE)是一种罕见的血管性肿瘤。它可累及皮肤、骨骼、结缔组织和实质器官,由于部分病例可能出现卡萨巴赫-梅里特现象,因此很难在早期做出明确诊断。2022 年 6 月 12 日,一名 19 个月大的男童以右髋关节屈曲 1 年多为主诉入住我科。我科为其实施了探查性开腹手术和盆腔病灶切除术,并切除了髂腰肌肌块。术中切除的肿瘤证实了卡波状血管内皮瘤的病理诊断。术后患儿生命体征平稳,恢复良好,血小板和凝血指标正常。KHE在临床上属于罕见病,目前世界上确诊病例数仍较少,病因和发病机制尚不清楚,可能导致疾病早期误诊和延误治疗。有必要继续收集相关病例,尽快统一标准治疗指南,降低病死率,提高病例的生活质量。
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Right iliopsoas kaposiform hemangioendothelioma: a case report
Kaposiform hemangioendothelioma (KHE) is a rare neoplasm of vascular origin. It may involve skin, bone, connective tissue, and parenchymal organs, and it is difficult to make a definite diagnosis in the early stage because Kasabach-Merritt phenomenon may occur in some cases. On June 12, 2022, a 19-month boy was admitted to our department with the chief complaint of flexion of the right hip joint for over 1 year. An exploratory laparotomy and pelvic lesion resection were conducted and the resection of the iliopsoas muscle mass was performed. The intraoperative resection of the neoplasm confirmed the pathological diagnosis of kaposiform hemangioendothelioma. The vital signs of the child were stable and recovered well after surgery, and the platelet and coagulation indices were normal. KHE is a rare disease in clinics, the number of confirmed cases in the world is still relatively few, and the etiology and mechanism of the disease are still unknown, which could result in misdiagnose and delayed treatment in the disease early stages. It is necessary to continue to collect relevant cases, to unify the standard treatment guidelines as soon as possible, to reduce the mortality rate, and to improve the quality of life of the cases.
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来源期刊
自引率
0.00%
发文量
32
审稿时长
9 weeks
期刊介绍: The Gazette is the official journal of the Egyptian Pediatric Association. The main purpose of the Gazette is to provide a place for the publication of high-quality papers documenting recent advances and new developments in both pediatrics and pediatric surgery in clinical and experimental settings. An equally important purpose of the Gazette is to publish local and regional issues related to children and child care. The Gazette welcomes original papers, review articles, case reports and short communications as well as short technical reports. Papers submitted to the Gazette are peer-reviewed by a large review board. The Gazette also offers CME quizzes, credits for which can be claimed from either the EPA website or the EPA headquarters. Fields of interest: all aspects of pediatrics, pediatric surgery, child health and child care. The Gazette complies with the Uniform Requirements for Manuscripts submitted to biomedical journals as recommended by the International Committee of Medical Journal Editors (ICMJE).
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