爱博斯坦畸形的临床表现和治疗。

4区医学 Q2 Biochemistry, Genetics and Molecular Biology Advances in experimental medicine and biology Pub Date : 2024-01-01 DOI:10.1007/978-3-031-44087-8_56

Nikolaus A Haas, David J Driscoll, Silke Rickert-Sperling

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引用次数: 0

摘要

埃布斯坦畸形是一种罕见的先天性心脏缺陷，占心脏畸形的比例不到 1%，每 21 万活产婴儿中约有 1 例。其特征是三尖瓣异常，即三尖瓣在右心室的位置低于正常位置。虽然主要是三尖瓣缺损，但右心室本身的结构通常也异常和衰弱（肌病）。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Clinical Presentation and Therapy of Ebstein Anomaly.

Ebstein anomaly is a rare congenital heart defect, accounting for less than 1% of cardiac malformations and occurring in approximately 1 out of 210,000 live births. It is characterized by an abnormality of the tricuspid valve, where the valve is positioned lower than normal in the right ventricle. Although primarily a tricuspid valve defect, the right ventricle itself is often structurally abnormal and weakened (myopathic).

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来源期刊

Advances in experimental medicine and biology 医学-医学：研究与实验

CiteScore

5.90

自引率

0.00%

发文量

465

审稿时长

2-4 weeks

期刊介绍： Advances in Experimental Medicine and Biology provides a platform for scientific contributions in the main disciplines of the biomedicine and the life sciences. This series publishes thematic volumes on contemporary research in the areas of microbiology, immunology, neurosciences, biochemistry, biomedical engineering, genetics, physiology, and cancer research. Covering emerging topics and techniques in basic and clinical science, it brings together clinicians and researchers from various fields.