临床视角:治疗脊髓肌肉萎缩症。

IF 12.1 1区 医学 Q1 BIOTECHNOLOGY & APPLIED MICROBIOLOGY Molecular Therapy Pub Date : 2024-08-07 Epub Date: 2024-06-18 DOI:10.1016/j.ymthe.2024.06.020
Molly A McPheron, Marcia V Felker
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引用次数: 0

摘要

脊髓性肌萎缩症是一种罕见的渐进性神经肌肉疾病,如不及时治疗,会导致患者逐渐虚弱,甚至死亡。自2016年以来,大量研究促使三种高成本、有效的治疗方法获得批准。这些疗法,即努西奈森、onasemnogene abeparvovec和利迪普兰,尚未进行过直接比较,在用药方面也存在不同的挑战。在这篇综述中,我们将讨论支持使用这些药物的证据、治疗选择过程、治疗后的监测、比较治疗的有限数据以及未来的研究和治疗方向。
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Clinical perspectives: Treating spinal muscular atrophy.

Spinal muscular atrophy is a rare and progressive neuromuscular disease that, without treatment, leads to progressive weakness and often death. A plethora of studies have led to the approval of three high-cost and effective treatments since 2016. These treatments, nusinersen, onasemnogene abeparvovec, and risdiplam, have not been directly compared and have varying challenges in administration. In this review, we discuss the evidence supporting the use of these medications, the process of treatment selection, monitoring after treatment, the limited data comparing treatments, as well as future directions for investigation and therapy.

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来源期刊
Molecular Therapy
Molecular Therapy 医学-生物工程与应用微生物
CiteScore
19.20
自引率
3.20%
发文量
357
审稿时长
3 months
期刊介绍: Molecular Therapy is the leading journal for research in gene transfer, vector development, stem cell manipulation, and therapeutic interventions. It covers a broad spectrum of topics including genetic and acquired disease correction, vaccine development, pre-clinical validation, safety/efficacy studies, and clinical trials. With a focus on advancing genetics, medicine, and biotechnology, Molecular Therapy publishes peer-reviewed research, reviews, and commentaries to showcase the latest advancements in the field. With an impressive impact factor of 12.4 in 2022, it continues to attract top-tier contributions.
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