后天性全身脂肪营养不良（泛发性）的一个不寻常病例。

IF 1.2 4区医学 Q3 DERMATOLOGY Pediatric Dermatology Pub Date : 2024-11-01 Epub Date: 2024-06-17 DOI:10.1111/pde.15668

Marlee Hill, Amanda S Weissman, Jason Hirshburg, Jeffrey D McBride, Hillary Lawrence

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引用次数: 0

摘要

获得性全身脂肪营养不良（AGL）是一种罕见的疾病，其特征是脂肪组织可变性缺失和并发代谢紊乱，通常在儿童或青少年时期发病。AGL 有三种亚型：泛发性脂膜炎（1 型）、自身免疫性疾病（2 型）和特发性（3 型）。本报告重点介绍了一例罕见的 AGL 1 型病例，患者是一名原本健康的 3 岁女性，表现为弥漫性红斑皮下结节、进行性脂肪萎缩，组织病理学检查结果为小叶泛发性炎。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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An unusual case of acquired generalized lipodystrophy (panniculitis variety).

Acquired generalized lipodystrophy (AGL) is a rare disease characterized by variable loss of adipose tissue and concurrent metabolic derangements, typically with childhood or adolescent onset. AGL has three subclassifications: panniculitis (type 1), autoimmune disease (type 2), and idiopathic (type 3). This report highlights a rare case of AGL type 1 in a previously healthy 3-year-old female who presented with diffuse erythematous subcutaneous nodules, progressive lipoatrophy, and histopathological findings of a lobular panniculitis.

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来源期刊

Pediatric Dermatology 医学-皮肤病学

CiteScore

3.20

自引率

6.70%

发文量

269

审稿时长

1 months

期刊介绍： Pediatric Dermatology answers the need for new ideas and strategies for today''s pediatrician or dermatologist. As a teaching vehicle, the Journal is still unsurpassed and it will continue to present the latest on topics such as hemangiomas, atopic dermatitis, rare and unusual presentations of childhood diseases, neonatal medicine, and therapeutic advances. As important progress is made in any area involving infants and children, Pediatric Dermatology is there to publish the findings.