Congenital Megalourethra Presented with Renal Anomalies

Megalourethra is a rare congenital disorder of male penile tissue and urethra, characterized by nonobstructive dilatation of the urethra, mainly classified into scaphoid and fusiform types. It is commonly associated with multisystem involvement including hydronephrosis, hydroureter, posterior urethral valves, and vertebral, anal, and cardiac anomalies. The isolated entity is rarely found. Urethroplasty is a management modality to treat megalourethra with the treatment of other associated anomalies. In this article, we are presenting a case of megalourethra associated with right hydronephrosis, Grade 3–4 vesicoureteral reflux, small left kidney, and posterior urethral valve.