儿童和成人分裂脐带畸形的表现和处理:病例系列。

IF 1.3 4区 医学 Q4 CLINICAL NEUROLOGY Child's Nervous System Pub Date : 2024-11-01 Epub Date: 2024-07-22 DOI:10.1007/s00381-024-06547-w
HariOm Vaja, Abhay Kapoor, Gurleen Kaur, Jividha Patwa, Jaimin Shah
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引用次数: 0

摘要

本研究的主要目的是加深人们对脊髓空洞症的了解,尤其侧重于成人发病病例,因为这种病例并不常见,也未得到充分阐明。此外,该研究还试图分析临床特征、诊断特点以及为控制病情而采取的手术干预措施。该回顾性病例系列旨在研究脊髓脊膜膨出症,这是一种影响脊髓的罕见先天性畸形。研究共纳入16名被诊断为脊髓纵隔的患者,包括13名儿童病例(平均年龄:7.6岁,年龄范围:5个月至13岁)和3名成人病例(平均年龄:36岁,年龄范围:26岁至48岁)。儿科病例中有 9 名女性和 4 名男性,成人病例中有 2 名男性和 1 名女性。研究设计包括对病历、影像学报告和手术结果进行全面审查,没有特定的纳入或排除标准。除一例病例外,其他病例均以手术治疗为主。手术治疗后,患者在疼痛控制、运动功能和膀胱控制方面均有明显改善。此外,其他研究结果表明,研究对象中存在硬脊膜外翻和椎体分节缺损。该回顾性系列病例揭示了儿童和成人背阔肌症的临床特征和手术效果。研究结果强调了手术治疗在缓解症状、提高运动协调能力和膀胱控制能力方面的重要性。
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Split Cord Malformation Presentation and Management in Pediatric and Adult Cases: a Case Series.

The primary purpose of this study was to enhance the understanding of diastematomyelia, with a particular focus on adult-onset cases, which are infrequent and not fully elucidated. Additionally, the study sought to analyse the clinical features, diagnostic characteristics, and surgical interventions employed to manage the condition. This retrospective case series aimed to investigate diastematomyelia, a rare congenital deformation affecting the spinal cord. The study included 16 patients diagnosed with diastematomyelia, consisting of 13 pediatric cases (mean age: 7.6 years, age range: 5 months to 13 years) and 3 adult cases (mean age: 36 years, age range: 26 to 48 years). Among the paediatric cases, 9 were females, and 4 were males, while the adult cohort comprised 2 males and 1 female. The study design involved a thorough review of medical records, imaging reports, and surgical outcomes without specific inclusion or exclusion criteria. Surgical intervention emerged as the primary treatment modality for all cases, except one. Following surgical intervention, significant improvements were observed in pain management, motor function, and bladder control. Furthermore, additional findings indicated the presence of Dural Ectasia and Vertebral segmentation defects among the study population. This retrospective case series sheds light on the clinical features and surgical outcomes of diastematomyelia in both pediatric and adult patients. The findings underscore the importance of surgical intervention in alleviating symptoms and enhancing motor coordination and bladder control.

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来源期刊
Child's Nervous System
Child's Nervous System 医学-临床神经学
CiteScore
3.00
自引率
7.10%
发文量
322
审稿时长
3 months
期刊介绍: The journal has been expanded to encompass all aspects of pediatric neurosciences concerning the developmental and acquired abnormalities of the nervous system and its coverings, functional disorders, epilepsy, spasticity, basic and clinical neuro-oncology, rehabilitation and trauma. Global pediatric neurosurgery is an additional field of interest that will be considered for publication in the journal.
期刊最新文献
Correction: Imaging features of pediatric meningiomas: emphasis on unusual locations. Correction: Occipital encephalocele: a retrospective analysis and assessment of post-surgical neurodevelopmental outcome. Radiographic severity is associated with worse executive function in metopic craniosynostosis. Occipital encephalocele: a retrospective analysis and assessment of post-surgical neurodevelopmental outcome. Vaulting further: cranial vault expansion for craniocerebral disproportion without primary craniosynostosis.
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