新生儿躯干先天性皮肤增生症:罕见病例报告。

IF 0.9 Q4 PUBLIC, ENVIRONMENTAL & OCCUPATIONAL HEALTH Pan African Medical Journal Pub Date : 2024-06-09 eCollection Date: 2024-01-01 DOI:10.11604/pamj.2024.48.52.43784
El Mouloua Ahmed, Aballa Najoua, Foura Salma, Kamili Elouafi Elaouni, Fouraiji Karima, Oulad Saiad Mohamed
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引用次数: 0

摘要

先天性皮肤增生症(ACC)是一种罕见的先天性疾病,是一种先天性皮肤缺陷,其特征是出生时所有皮肤层均缺失。最常见的表现是头皮顶端出现小面积红斑性溃疡或疤痕样脱发性外皮损伤。然而,躯干大面积皮肤增生症却极为罕见。临床和放射学评估确定了适当的治疗方法。我们在此报告了一例罕见的先天性躯干大面积皮肤增生症病例,该病例发生在一名男性新生儿身上,采用 1%磺胺嘧啶银敷料进行治疗,约一个月后伤口完全愈合。该报告强调,保守治疗是治疗非头皮大面积 ACC 的一种高效实用的方法。
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Aplasia cutis congenita of the trunk in a newborn: a rare case report.

Aplasia cutis congenita (ACC) is a rare congenital disorder defined as a congenital skin defect, characterized by the absence of all skin layers at birth. The most frequent presentation is a small erythematous ulcerated or scar-like alopecic ectodermal lesion on the scalp vertex. However, extensive cutis aplasia of the trunk is extremely uncommon. Clinical and radiological evaluation defined the appropriate treatment. We herein report a rare case of a large aplasia cutis congenita of the trunk occurring in a male newborn managed with sulfadiazine silver 1% dressing, complete healing was achieved in about a month. The report highlights that conservative treatment is a highly effective and practical option for managing non-scalp extensive ACC.

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来源期刊
Pan African Medical Journal
Pan African Medical Journal PUBLIC, ENVIRONMENTAL & OCCUPATIONAL HEALTH-
CiteScore
1.80
自引率
0.00%
发文量
691
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