治疗 Vohwinkel 综合征的长期手术成功：病例报告

Q4 Medicine JBJS case connector Pub Date : 2024-11-07 eCollection Date: 2024-10-01 DOI:10.2106/JBJS.CC.24.00251

Kirby W Bonvillain, Andrew B Rees, Katherine D Drexelius, Ryan Serbin, Michael W Aversano, R Glenn Gaston

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引用次数: 0

摘要

病例Vohwinkel 综合征是一种罕见的遗传性疾病，以角质化缺陷为特征。这种疾病可能会出现数字收缩带（假性畸形），从而导致自体截肢。手术切除是治疗假性股骨头坏死的唯一方法，但这种方法容易复发。我们为您介绍一名患有假性湿疣的 10 岁男孩，他的右手长指和小指远端指间关节处患有假性湿疣。他接受了 180 度带状切除术和 Z 形成形术：结论：自 8 年前开始治疗以来，他已接受了 5 次收缩带治疗，仅有 1 次复发。我们相信这一成功至少部分归功于 Upton 所描述的技术。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Long-Term Surgical Success in Treating Vohwinkel Syndrome: A Case Report.

Case: Vohwinkel syndrome is a rare, inherited condition marked by defective keratinization. The disorder may feature digital constriction bands (pseudoainhum) which can lead to autoamputation. Surgical excision is the only treatment of pseudoainhum; however, it is fraught with recurrence. We present a 10-year-old boy with pseudoainhum of the right long and small fingers at the distal interphalangeal joints. He underwent 180-degree band excision and z-plasty.

Conclusion: Since establishing care 8 years ago, he has undergone treatment of 5 constriction bands with only 1 recurrence. We believe this success can at least be partially attributed to the technique described by Upton.

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来源期刊

JBJS case connector Medicine-Medicine (all)

CiteScore

0.60

自引率

0.00%

发文量

319

期刊介绍： JBJS Case Connector helps improve patient care by providing the medical community with a journal that harnesses technology to provide information tools for discovery and reporting of unusual musculoskeletal problems, findings, treatment, and outcomes. Co-edited by Thomas W. Bauer, MD, PhD, and Ronald W. Lindsey, MD, JBJS Case Connector assists orthopaedic surgeons in the search for precedents, connections, and trends in their efforts to improve patient care. Using this unique journal, surgeons can find the commonalities between cases, benefit from the experience of their peers, and filter case information by many important variables in order to provide the best possible care for orthopaedic patients. This cross-referenced online journal includes thousands of orthopaedic case reports. It compiles symptoms, conditions, and demographic details to empower surgeons to find cases similar to theirs. Surgeons can mine the database to reveal emerging trends and identify patterns, distinguishing between truly rare cases and repeated, related single instances of a larger problem. The JBJS Case Connector Image Quiz feature provides interactive quizzes based on images from content published by JBJS and includes a discussion area for further exploration of ideas and concepts. The JBJS Image Quiz app for iPad and iPhone is available in the App Store. Contributions to JBJS Case Connector are welcomed from anywhere in the world and are considered on their merits. Articles must be written in English and should be submitted as outlined in the Instructions to Authors. All authors must abide by the JBJS ethics policies and all submissions to JBJS Case Connector are covered by the JBJS embargo policy.