一例罕见的22岁侧眼眶上皮样血管内皮瘤病例。

IF 1 Q3 MEDICINE, GENERAL & INTERNAL Cureus Pub Date : 2025-01-07 eCollection Date: 2025-01-01 DOI:10.7759/cureus.77084
Jeffrey Abdullah, Amarpreet Kaur Chohan, Sadiq Mawji, Pradyumna Naredla, Matthew R Idle
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摘要

上皮样血管内皮瘤(EHE)是一种罕见的血管肿瘤,其特征是血管内皮细胞和内皮前细胞的增殖。患病率不到百万分之一。它主要见于四肢的软组织,但也可发生在骨、脑、肝、肺和淋巴结。头颈部的EHE非常罕见。头颈部最常见的发生部位是下颌下区域。据我们所知,在轨道上只报道了4例EHE。我们在此报告一位22岁女性右眼眶外侧壁EHE的罕见病例,并描述其临床表现、组织病理学、鉴别诊断和治疗。EHEs表现出恶性和复发的可能性,但转移仍然罕见。由于其明显的恶性和复发的可能性,完全切除和定期长期随访将是适当的治疗方案。
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A Rare Case of Epithelioid Haemangioendothelioma of the Lateral Orbit in a 22-Year-Old Patient.

Epithelioid haemangioendothelioma (EHE) is a rare vascular neoplasm characterised by proliferation of vascular endothelial and pre-endothelial cells. The prevalence is less than one in a million people. It is principally observed in the soft tissues of the extremities but can also occur in the bone, brain, liver, lung and lymph nodes. EHE in the head and neck region is very rare. The most common site of occurrence in the head and neck is the submandibular region. To the best of our knowledge, there are only four cases of EHE reported in the orbit. We herein present the unusual case of a 22-year-old female patient with an EHE of the lateral wall of the right orbit and describe the clinical findings, histopathology, differential diagnoses and treatment. EHEs exhibit the potential for malignancy and recurrence, but metastasis remains rare. Due to its noticeable potential for malignancy and recurrence, complete excision and regular long-term follow-up would be the appropriate treatment protocol.

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