[结节病的皮肤表现]。

IF 0.7 Dermatologie (Heidelberg, Germany) Pub Date : 2025-04-01 Epub Date: 2025-03-11 DOI:10.1007/s00105-025-05491-3
Henning Klapproth, Torsten Kubacki, Mario Fabri, Esther von Stebut
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引用次数: 0

摘要

结节病是一种非传染性、炎症性多系统疾病,以特发性肉芽肿形成为特征。结节病的发病机制仍然只是部分了解,尽管各种临床危险因素和外部触发因素已经确定,以及维持th1介导的免疫反应。在临床上,结节病可表现为组织学检查观察到的与结节样肉芽肿相关的特异性表现,也可表现为非特异性表现。组织学是诊断的关键。在皮肤结节病的病例中,必须评估是否累及全身。治疗方法是针对受影响最严重的器官量身定制的。对于皮肤结节病,治疗方案因临床表现而异,包括局部治疗和全身干预。这些药物包括皮质类固醇和其他免疫抑制剂或免疫调节剂。
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[Cutaneous manifestations of sarcoidosis].

Sarcoidosis is a noninfectious, inflammatory multisystem disorder characterized by the idiopathic formation of granulomas. The pathogenesis of sarcoidosis remains only partially understood, although various clinical risk factors and extrinsic triggers have been identified, alongside a maintained Th1-mediated immune response. Clinically, sarcoidosis can present with specific manifestations associated with sarcoidal granulomas observable in histological examinations, as well as nonspecific manifestations. Histology is pivotal for diagnosis. In cases of cutaneous sarcoidosis, systemic involvement must be evaluated. Therapeutic approaches are tailored to the most affected organ. For cutaneous sarcoidosis, treatment options vary based on clinical findings and include local therapies as well as systemic interventions. These encompass corticosteroids and other immunosuppressive or immunomodulatory agents.

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