胸膜孤立性纤维瘤引起的癫痫:多吉-波特综合征的一种不寻常的表现。

IF 0.6 Q3 MEDICINE, GENERAL & INTERNAL BMJ Case Reports Pub Date : 2025-04-02 DOI:10.1136/bcr-2024-262770
Awdhah Alhajeri, Syed Faisal Hashmi, Eustace Fontane
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引用次数: 0

摘要

doge - potter综合征(DPS)是一种罕见的由孤立性纤维性肿瘤(SFTs)引起的低胰岛素血症性低血糖的疾病。本病例报告详细介绍了一名中年男性(40-65岁)在经历晕厥和血管迷走神经性发作后诊断为DPS的治疗方法,这导致在胸膜中发现了一个大肿块。在各种诊断检查确认SFT后,由于反复发作和严重低血糖,患者在手术前需要抗惊厥药物治疗和葡萄糖输注。手术切除肿瘤后,低血糖和抗惊厥药物的需求都得到了解决。本病例强调了在不明原因低血糖和胸内肿块患者中考虑DPS的重要性。结论:手术切除是伴有DPS的SFTs的首选治疗方法,预后良好,并强调需要定期随访以监测潜在的复发。
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Seizures caused by a solitary fibrous tumour of the pleura: an unusual presentation of Doege-Potter syndrome.

Doege-Potter syndrome (DPS) is a rare condition that causes hypoinsulinaemic hypoglycaemia due to solitary fibrous tumours (SFTs). This case report details the treatment of a man in middle adulthood (ages 40-65) diagnosed with DPS after experiencing syncope and vasovagal episodes, which led to the discovery of a large mass in the pleura. Following various diagnostic tests confirming the SFT, the patient required anticonvulsant therapy and glucose infusions due to recurrent seizures and severe hypoglycaemia prior to surgery. After the surgical removal of the tumour, both hypoglycaemia and the need for anticonvulsants were resolved. This case highlights the importance of considering DPS in patients with unexplained hypoglycaemia and intrathoracic masses. It concludes that surgical resection is the preferred treatment for SFTs associated with DPS, offering a favourable prognosis, and emphasises the need for regular follow-up to monitor for potential recurrence.

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来源期刊
BMJ Case Reports
BMJ Case Reports Medicine-Medicine (all)
CiteScore
1.40
自引率
0.00%
发文量
1588
期刊介绍: BMJ Case Reports is an important educational resource offering a high volume of cases in all disciplines so that healthcare professionals, researchers and others can easily find clinically important information on common and rare conditions. All articles are peer reviewed and copy edited before publication. BMJ Case Reports is not an edition or supplement of the BMJ.
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