M. Jarraya , R. Gargouri , H. Fendri , A. Makni , S. Charfeddine , L. Abid
{"title":"压缩血管环:1例报告及文献复习","authors":"M. Jarraya , R. Gargouri , H. Fendri , A. Makni , S. Charfeddine , L. Abid","doi":"10.1016/j.acvdsp.2023.07.051","DOIUrl":null,"url":null,"abstract":"<div><h3>Introduction</h3><p>Double aortic arch<span><span> (DAA) is one of the classes of congenital anomalies of the </span>aortic arch<span> system called vascular ring.</span></span></p><p>Abnormal circular formation of blood vessels are incircled around the trachea and oesophagus resulting in airway compression.</p></div><div><h3>Objective</h3><p>We report a case of a 2-month-old infant that was born at full term and had no medical or surgical history<span> who presented with progressive stridor and dyspnea reported by the parents.</span></p></div><div><h3>Methods</h3><p>On examination, we noticed a stridor, with suprasternal and intercostal recessions.</p><p><span><span>Oxygen saturations on room air was 93% and chest </span>auscultation<span> revealed bilateral transmitted stridor. A chest X-ray was normal. Echocardiography was performed and revealed a left-right shunting </span></span>atrial septal defect<span> with dilated right chambers, in addition to a persistent ductus arteriosus with a doubt on double aortic arch.</span></p></div><div><h3>Results/Expected results</h3><p><span>Thoracic computed tomography (CT) was performed and a vascular ring, consisting of a double aortic arch, was found compressing and narrowing the trachea (</span><span>Figure 1</span>).</p><p>The CT allowed confirmation of the anomaly, its location and the severity of airway and oesophageal compression.</p><p>Three-dimensional reconstruction helped to plan surgical intervention.</p><p>The patient was then referred to the cardiothoracic surgery.</p><p>The intervention consisted of resecting the minor arch freeing the trachea.</p></div><div><h3>Conclusion/Perspectives</h3><p>DAA is a rare issue mostly diagnosed in childhood due to symptoms related to oesophageal and/or tracheal compression and obstruction.</p><p>It can be associated to cardiac malformations including ventricular septal defect and Fallot's tetralogy.</p><p>Left untreated, it may lead to significant morbidity and mortality from airway obstruction.</p><p><span>Surgical repair remains the mainstay of treatment and is indicated for patients with symptoms of airway or digestive compression or as a supplementary procedure </span>in patients undergoing other cardiac surgery.</p><p>The principle of surgery is to relieve the vascular compression on the trachea and/or esophagus by the division of the lesser arch.</p></div>","PeriodicalId":8140,"journal":{"name":"Archives of Cardiovascular Diseases Supplements","volume":"15 4","pages":"Page 296"},"PeriodicalIF":18.0000,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"A compressive vascular ring: A case report and review of literature\",\"authors\":\"M. Jarraya , R. Gargouri , H. Fendri , A. Makni , S. Charfeddine , L. Abid\",\"doi\":\"10.1016/j.acvdsp.2023.07.051\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div><h3>Introduction</h3><p>Double aortic arch<span><span> (DAA) is one of the classes of congenital anomalies of the </span>aortic arch<span> system called vascular ring.</span></span></p><p>Abnormal circular formation of blood vessels are incircled around the trachea and oesophagus resulting in airway compression.</p></div><div><h3>Objective</h3><p>We report a case of a 2-month-old infant that was born at full term and had no medical or surgical history<span> who presented with progressive stridor and dyspnea reported by the parents.</span></p></div><div><h3>Methods</h3><p>On examination, we noticed a stridor, with suprasternal and intercostal recessions.</p><p><span><span>Oxygen saturations on room air was 93% and chest </span>auscultation<span> revealed bilateral transmitted stridor. A chest X-ray was normal. Echocardiography was performed and revealed a left-right shunting </span></span>atrial septal defect<span> with dilated right chambers, in addition to a persistent ductus arteriosus with a doubt on double aortic arch.</span></p></div><div><h3>Results/Expected results</h3><p><span>Thoracic computed tomography (CT) was performed and a vascular ring, consisting of a double aortic arch, was found compressing and narrowing the trachea (</span><span>Figure 1</span>).</p><p>The CT allowed confirmation of the anomaly, its location and the severity of airway and oesophageal compression.</p><p>Three-dimensional reconstruction helped to plan surgical intervention.</p><p>The patient was then referred to the cardiothoracic surgery.</p><p>The intervention consisted of resecting the minor arch freeing the trachea.</p></div><div><h3>Conclusion/Perspectives</h3><p>DAA is a rare issue mostly diagnosed in childhood due to symptoms related to oesophageal and/or tracheal compression and obstruction.</p><p>It can be associated to cardiac malformations including ventricular septal defect and Fallot's tetralogy.</p><p>Left untreated, it may lead to significant morbidity and mortality from airway obstruction.</p><p><span>Surgical repair remains the mainstay of treatment and is indicated for patients with symptoms of airway or digestive compression or as a supplementary procedure </span>in patients undergoing other cardiac surgery.</p><p>The principle of surgery is to relieve the vascular compression on the trachea and/or esophagus by the division of the lesser arch.</p></div>\",\"PeriodicalId\":8140,\"journal\":{\"name\":\"Archives of Cardiovascular Diseases Supplements\",\"volume\":\"15 4\",\"pages\":\"Page 296\"},\"PeriodicalIF\":18.0000,\"publicationDate\":\"2023-09-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Archives of Cardiovascular Diseases Supplements\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://www.sciencedirect.com/science/article/pii/S1878648023002720\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q4\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Archives of Cardiovascular Diseases Supplements","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S1878648023002720","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"Medicine","Score":null,"Total":0}
A compressive vascular ring: A case report and review of literature
Introduction
Double aortic arch (DAA) is one of the classes of congenital anomalies of the aortic arch system called vascular ring.
Abnormal circular formation of blood vessels are incircled around the trachea and oesophagus resulting in airway compression.
Objective
We report a case of a 2-month-old infant that was born at full term and had no medical or surgical history who presented with progressive stridor and dyspnea reported by the parents.
Methods
On examination, we noticed a stridor, with suprasternal and intercostal recessions.
Oxygen saturations on room air was 93% and chest auscultation revealed bilateral transmitted stridor. A chest X-ray was normal. Echocardiography was performed and revealed a left-right shunting atrial septal defect with dilated right chambers, in addition to a persistent ductus arteriosus with a doubt on double aortic arch.
Results/Expected results
Thoracic computed tomography (CT) was performed and a vascular ring, consisting of a double aortic arch, was found compressing and narrowing the trachea (Figure 1).
The CT allowed confirmation of the anomaly, its location and the severity of airway and oesophageal compression.
Three-dimensional reconstruction helped to plan surgical intervention.
The patient was then referred to the cardiothoracic surgery.
The intervention consisted of resecting the minor arch freeing the trachea.
Conclusion/Perspectives
DAA is a rare issue mostly diagnosed in childhood due to symptoms related to oesophageal and/or tracheal compression and obstruction.
It can be associated to cardiac malformations including ventricular septal defect and Fallot's tetralogy.
Left untreated, it may lead to significant morbidity and mortality from airway obstruction.
Surgical repair remains the mainstay of treatment and is indicated for patients with symptoms of airway or digestive compression or as a supplementary procedure in patients undergoing other cardiac surgery.
The principle of surgery is to relieve the vascular compression on the trachea and/or esophagus by the division of the lesser arch.
期刊介绍：
Archives of Cardiovascular Diseases Supplements is the official journal of the French Society of Cardiology. The journal publishes original peer-reviewed clinical and research articles, epidemiological studies, new methodological clinical approaches, review articles, editorials, and Images in cardiovascular medicine. The topics covered include coronary artery and valve diseases, interventional and pediatric cardiology, cardiovascular surgery, cardiomyopathy and heart failure, arrhythmias and stimulation, cardiovascular imaging, vascular medicine and hypertension, epidemiology and risk factors, and large multicenter studies. Additionally, Archives of Cardiovascular Diseases also publishes abstracts of papers presented at the annual sessions of the Journées Européennes de la Société Française de Cardiologie and the guidelines edited by the French Society of Cardiology.
京公网安备 11010802042870号
京ICP备2023020795号-1
分享
求助内容：
应助结果提醒方式：
扫码关注我们
