Inflammatory myofibroblastic tumor of the ureter in a paediatric patient

Inflammatory myofibroblastic tumor (IMT) is a rare soft-tissue neoplasm which has been described in a variety of locations. In the urogenital system, it occurs mainly in the bladder and the kidney. IMT arising from the ureter is exceedingly rare. We report an exceptional case of IMT arising from the ureteric submucosa in a three-year-old female child. The patient presented with pan-hematuria and no other symptoms. Urinalysis revealed numerous red blood cells, culture was negative for infection. A CT Urogram showed the lesion was involving most of the ureter. A left radical nephroureterectomy was performed, and she has remained well to date. Ureteral IMT is extremely rare and often asymptomatic, which can result in a delayed diagnosis. Radical excision is the best therapeutic approach with excellent survival outcomes.