以胸膜肺滑膜肉瘤为表现的反复气胸

Q4 Medicine Revista de Patologia Respiratoria Pub Date : 2012-04-01 DOI:10.1016/S1576-9895(12)70142-X

M. Estors , P. Rinaldi , C. Gaspar , F. Sánchez , R. Esturi , J.M. Galbis

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引用次数: 0

摘要

滑膜肉瘤是一种软组织肿瘤，多发于中青年，性别分布无差异。90%的病例位于四肢。胸膜肺原发性滑膜肉瘤(SSPP)非常罕见，约占肺部肿瘤的0.1%。在大多数情况下，SSPP表现为咳嗽和/或咯血，而气胸是一种罕见的表现形式。预后通常较差，局部复发风险高。生存率取决于手术治疗，是肿瘤完全切除的主要预测因素。手术是治疗的选择，其次是化疗、放疗或两者兼而有之。我们报告一例胸膜肺滑膜肉瘤并发气胸。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Neumotórax de repetición como presentación de sarcoma sinovial pleuropulmonar

Synovial sarcomas are a soft-tissue neoplasms which affects young and middle-aged people, with no difference in distribution between sexes. They are located in the extremities in the 90% of the cases.

Pleuropulmonary primary synovial sarcoma SSPP is very unusual, constitutes 0.1% of pulmonary tumors. In most cases the SSPP present themselves with cough and / or hemoptysis whereas pneumothorax is an uncommon form of presentation.

Prognosis is usually poor, they present high risk of local recurrence. The survival rate depends on the surgical treatment, being the complete tumor resection the main predicting factor. Surgery is the treatment of choice followed by chemotherapy, radiotherapy or both.

We present a case report of a pleuropulmonary synovial sarcoma which presented with pneumothorax.

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来源期刊

Revista de Patologia Respiratoria Medicine-Pulmonary and Respiratory Medicine

CiteScore

0.30

自引率

0.00%

发文量

期刊介绍： Revista de Patología Respiratoria is the scientific journal of the Madrilenian Pulmonology and Thoracic Surgery Society (Neumomadrid). It will consider those original articles related to Pulmonology, Thoracic Surgery and all other related sciences for their possible publication. Other types of articles such as reviews, editorials, special articles, scientific letters and letters to the editor are also published in the journal. It is a quarterly Journal that publishes a total of 4 issues, which contain these types of articles to different extents. All publications submitted will always undergo a peer review and a final decision will be made according to comments from the expert reviewers and members of the Editorial Board. The Journal is published both in Spanish and English. Therefore, the submission of manuscripts written in either Spanish or English is welcome.