胃癌合并卡塔赫纳综合征的手术治疗一例

S. Afanasyev, A. Dobrodeev, D. Kostromitsky, Yu. V. Rudyk, M. Y. Grishchenko, E. S. Drozdov, E. N. Samtsov, U. Urmonov
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引用次数: 0

摘要

Kartagener综合征(CS)是一种罕见的常染色体隐性遗传病,是原发性纤毛运动障碍(PCD)的一部分,其特征是三征综合征,包括支气管扩张、多分泌性鼻窦炎和胸腔和腹腔内部器官的完全镜像排列(倒位)。在大多数患者中,肺部支气管扩张从生命的最初几年开始发展并随着时间的推移而发展。诊断迟缓导致疾病预后不良,并诱发持续违反外呼吸功能的发展。大多数情况下,CS患者从儿童早期就由医生和肺科医生观察到,因为呼吸道感染由于呼吸道纤毛上皮的异常,通常需要每年在专门的医疗机构住院。然而,到目前为止,对于这类患者的管理和治疗还没有普遍接受的建议。这篇文章描述了一个新诊断的CS在一个老年患者接受手术治疗的胃癌。尽管支气管肺系统的病变明显,但患者的围手术期进展相对令人满意,并没有增加住院时间。
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A rare case of surgical treatment of a patient with gastric cancer with Cartagener syndrome
Kartagener Syndrome (CS) is a rare autosomal recessive disease that is a part of primary ciliary dyskinesia (PCD), and is characterized by a triad of syndrome including bronchiectasis, polysinusitis and a complete mirror arrangement of the internal organs of the chest and abdominal cavities (situs inversus). In most patients, bronchiectasis in the lungs develops from the first years of life and progresses in time. The tardy diagnostic leads to a poor prognosis of the disease and adduce the development of persistent violations of the function of external respiration. Most often, patients with CS are observed by physicians and pulmonologists from early childhood, since respiratory infections often require annual hospitalization in specialized medical institutions due to abnormalities of the ciliary epithelium of the respiratory tract. However, to date, there are no generally accepted recommendations for the management and treatment of patients in this category. This article describes the case of a newly diagnosed CS in an older patient undergoing surgical treatment for gastric cancer. Despite the pronounced concomitant pathology on the part of the bronchopulmonary system, the perioperative period in the patient proceeded relatively satisfactorily and did not entail an increase in the length of hospitalization.
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来源期刊
CiteScore
0.30
自引率
0.00%
发文量
40
审稿时长
8 weeks
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