胎儿泌尿病理学

P Diallo, F Jacquemard, F Kieffer, V Mirlesse, S Romand, P Thulliez
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引用次数: 1

摘要

肾发育不全是指由于肾后胚芽发育不全而导致的一个或两个肾脏缺失。小儿肾脏或肝肾多囊瘤是一种常染色体隐性遗传性疾病,约占肾脏或肝肾畸形泌尿系统疾病的1%。它的特征是集合小管的微多囊性扩张。多囊性发育不良是由于后肾胚胎发育异常引起的,约占先天性尿路畸形的1%。大多数情况下,这种异常是单侧的,由肾容量异常增加来定义。肾盂增生是指肾盂异常扩张。肾积水是最常见的尿路疾病,在先天性肾脏和尿路畸形中发生率为30 - 50%。它的特点是肾盂和肾盏扩张。大输尿管是指输尿管异常扩张。在巨大膀胱疾病中,膀胱容量可能随检查而变化,或在单次检查期间,取决于泌尿病理学。主要病因是后输尿管异常和梅干-腹部综合征。
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Pathologie urinaire fœtale

Renal agenesia refers to the lack of one or the two kidneys, arising from an agenesis of the metanephros blastema. Paediatric renal or hepato-renal polycystoma is an autosomic recessive hereditary disease concerning 1% of renal or hepato-renal malformative uropathies. It is characterized by a micro-polycystic ectasy of collecting tubules. Polycystic dysplasia is due to abnormal metanephros embryonic development, and represents about 1% of congenital malformative uropathies. Most of the time, such abnormality is unilateral and is defined by an abnormally increased renal volume. Pyelectasia refers to abnormal dilatation of the renal pelvis. Hydronephrosis is the most frequent urinary tract disorder, with an occurrence rate of 30 to 50% among congenital malformations of the kidney and the urinary tract. It is characterized by the dilatation of renal pelvis and calyxes. Megalo-ureter refers to abnormally dilated ureter. In the mega bladder disease, the bladder capacity may vary from an examination to another, or during a single examination, depending on the urinary pathology. Main aetiologies are the posterior ureter abnormalities, and the Prune- Belly syndrome.

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