{"title":"先天性心脏病肺动脉高压","authors":"A. A. Frogoudaki, M. A. Gatzoulis","doi":"10.1002/cce2.74","DOIUrl":null,"url":null,"abstract":"<div>\n \n <p>The number of patients with pulmonary arterial hypertension related to congenital heart disease (PAH-CHD) seen in specialist centers continues to increase. The extreme end of the spectrum, namely Eisenmenger's syndrome, is further compromised with chronic cyanosis and multiorgan disease, In this review we present the current knowledge on definition, prevalence, pathophysiology, classification, diagnosis, and treatment of this entity that has great impact on CHD patients’ life.</p>\n </div>","PeriodicalId":100331,"journal":{"name":"Continuing Cardiology Education","volume":"4 1","pages":"23-33"},"PeriodicalIF":0.0000,"publicationDate":"2018-07-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1002/cce2.74","citationCount":"1","resultStr":"{\"title\":\"Pulmonary arterial hypertension in congenital heart disease\",\"authors\":\"A. A. Frogoudaki, M. A. Gatzoulis\",\"doi\":\"10.1002/cce2.74\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div>\\n \\n <p>The number of patients with pulmonary arterial hypertension related to congenital heart disease (PAH-CHD) seen in specialist centers continues to increase. The extreme end of the spectrum, namely Eisenmenger's syndrome, is further compromised with chronic cyanosis and multiorgan disease, In this review we present the current knowledge on definition, prevalence, pathophysiology, classification, diagnosis, and treatment of this entity that has great impact on CHD patients’ life.</p>\\n </div>\",\"PeriodicalId\":100331,\"journal\":{\"name\":\"Continuing Cardiology Education\",\"volume\":\"4 1\",\"pages\":\"23-33\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2018-07-27\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://sci-hub-pdf.com/10.1002/cce2.74\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Continuing Cardiology Education\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://onlinelibrary.wiley.com/doi/10.1002/cce2.74\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Continuing Cardiology Education","FirstCategoryId":"1085","ListUrlMain":"https://onlinelibrary.wiley.com/doi/10.1002/cce2.74","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Pulmonary arterial hypertension in congenital heart disease
The number of patients with pulmonary arterial hypertension related to congenital heart disease (PAH-CHD) seen in specialist centers continues to increase. The extreme end of the spectrum, namely Eisenmenger's syndrome, is further compromised with chronic cyanosis and multiorgan disease, In this review we present the current knowledge on definition, prevalence, pathophysiology, classification, diagnosis, and treatment of this entity that has great impact on CHD patients’ life.