Left ventricular noncompaction associated with mitral valve prolapse and severe mitral regurgitation

Left ventricular non compaction (LVNC) cardiomyopathy is rare. Associated valvular lesions are still remote and they can complicate the underlying myocardial dysfunction. Echocardiographic diagnosis is well established. We are reporting a case of LVNC who presented with class III NYHA due to mitral valve prolapse with severe mitral regurgitation and severe LV dysfunction who was successfully operated and found asymptomatic with near normal LV function during 18 months follow up. This report is to stress that surgical management is feasible when indicated in cases of LVNC with acceptable outcomes.