一例因黏液性水肿而发生心脏填塞的滑脱患者的麻醉处理

S. Ural, Dilruba Güngör, Ömer Faruk Gülaştı
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摘要

身材矮小,身体矮小,发育不成比例的侏儒症。这种罕见的遗传病是常染色体显性遗传,常见于妇女,每10000例活产婴儿中有0.5-1.5例。软骨内成骨不足和正常骨膜成骨障碍是其特征性表现;患者有骨畸形和全身异常寰枢脱位(AAD)可能同时存在于软骨发育不全患者中,可能是新生的,可能是手术后(枕骨大孔减压),也可能是由于齿状突异常(齿状突缺失)。鉴于解剖和生理上的限制以及可能涉及的多系统,软骨发育不全合并AAD患者的麻醉管理为麻醉医师提供了一个复杂的命题在这个病例报告中,我们的目的是在文献的背景下介绍一个软骨发育不全患者的全身麻醉管理,该患者因心包积液后发生的心脏填塞而手术。病例报告
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Anesthesia Management in an Acondroplasic Patient Developing Cardiac Tamponade Due to Myxedema
dwarfism with short stature, short body and disproportionate development. This rare genetic disease, which is 0.5-1.5 in 10000 live births, is autosomal dominant inheritance and is common in women. Deficiency of endochondral bone formation and normal periostal bone formation disorder are characteristic; patients have bone deformities and systemic anomalies.1 Atlantoaxial dislocation (AAD) may concurrently exist in achondroplastic patients either de novo, following surgery (foramen magnum decompression) or due to odontoid abnormalities (os odontoideum). Anesthetic management of achondroplastic patients with coexisting AAD offers a complex proposition for anesthesiologists in view of the anatomical and physiological constraints and the possible multisystem involvement.2 In this case report, we aimed to present general anesthesia management in the context of the literature in an achondroplasic patient who was operated due to cardiac tamponade developed after pericardial effusion. CASE REPORT
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