A Rare Case of Evans Syndrome Associated With Optic Neuritis: A Case Report

Purpose: To report a case of Evans Syndrome associated with severe optic neuritis. Case Report: HAF, male, 26 years old, diagnosed with Evans Syndrome at the age of nine, with a history of headache and right eye pain with worsening movement. Fifteen days after the initial condition, visual clouding and decreased visual acuity began. Ophthalmological examination revealed visual acuity of 20/200 in the right eye with progressive worsening as the condition progressed; and 20/20 in the left eye. Visual field with absolute scotomata in the right eye and relative and absolute scotomatous points in all quadrants of the left eye. Gluorescein angiography findings included optic disc attenuation, without hyperfluorescent lesions. Conclusion: Evans Syndrome is a pathology that is gradually expanding in the field of clinical research, which has allowed new concepts related to pathogenesis and association with other comorbid conditions. In this case, we report the association with unilateral Optic Neuritis, responsible for progressive visual loss. Such knowledge aggregates the scientific community and translates into the need for an early multidisciplinary approach.