克罗恩病患者持续发热:成人斯蒂尔氏病

L. Carrión-Martín , G. Pérez-Rial , A.I. Hernando-Alonso , L. Menchén-Viso , J. Pajares-Díaz , F.J. López-Longo , M. Valerio , M.J. Penalva-Moreno , I. Marín-Jimenez
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引用次数: 0

摘要

肠外表现是克罗恩病(CD)的常见表现。成人发病的斯蒂尔氏病是一种罕见的疾病,表现为关节炎和关节痛,高(>39°C)和持续发热、皮疹、喉咙痛、淋巴结病和肝脾肿大。文献中只有3例成人发病的斯蒂尔氏病表现为乳糜泻患者。我们描述了一个新的病例成人发病斯蒂尔氏病相关的结缔组织病。虽然不常见,但重要的是要了解这种疾病的鉴别诊断关节痛和高热的乳糜泻患者。
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Fiebre persistente en paciente con enfermedad de Crohn: enfermedad de Still del adulto

Extra-intestinal manifestations are frequent in Crohn's disease (CD). Adult onset Still's disease is a rare disease presenting with arthritis and arthralgia, high ( > 39 °C) and persistent fever, rash, sore throat, lymphadenopathies and hepatosplenomegaly. There are only 3 cases in literature of adult onset Still's disease presenting in CD patients. We describe a new case of adult onset Still's disease associated to connective tissue disease. Although infrequent, it is important to become aware of this disease for the differential diagnosis of arthralgia and high fever in CD patients.

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