航空颗粒细胞瘤的临床病理特征和发病机制:慢性烟草粘膜刺激的合理神经来源。

Jesús Machuca-Aguado, Fernando Cózar-Bernal, Enrique Rodríguez-Zarco, Juan José Ríos-Martin, Miguel Ángel Idoate Gastearena
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引用次数: 0

摘要

颗粒细胞瘤(GCT)是一种源自雪旺氏细胞的病变,可发生于任何部位,但在主气道少见。我们报告了5例气道GCT的单中心系列病例,所有患者均为吸烟者。GCT的发病机制尚不清楚。描述了吸烟习惯与GCT的关系。我们假设吸烟可能导致呼吸道GCT和其他呼吸神经肿瘤,作为支气管小神经慢性损伤的反应性或肿瘤性过程。支持这一解释的事实是,烟草烟雾在慢性阻塞性肺疾病的背景下产生周围神经系统的参与。有临床和实验的理由假设,烟草烟雾可以产生与沃勒氏变性相关的雪旺细胞增殖,从而产生各种雪旺细胞肿瘤。此外,这种刺激慢性假说可以解释一些患者的多中心特征。随访显示患者行为良好,无复发。建议对GCT采取保守治疗。
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Clinicopathological Characteristics and Pathogenesis of Granular Cell Tumours of the Airways: A Plausible Neural Origin Through Chronic Tobacco Mucosa Irritation.
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CiteScore
4.40
自引率
6.10%
发文量
121
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