[刚果共和国布拉柴维尔大学医院一名儿童的宫颈肿瘤]。

Medecine tropicale et sante internationale Pub Date : 2023-03-14 eCollection Date: 2023-03-31 DOI:10.48327/mtsi.v3i1.2023.340

Alexis Elira Dokékias, Firmine Olivia Galiba Atipo Tsiba, Fortuné Bissiko, Antoine Martin

{"title":"[刚果共和国布拉柴维尔大学医院一名儿童的宫颈肿瘤]。","authors":"Alexis Elira Dokékias, Firmine Olivia Galiba Atipo Tsiba, Fortuné Bissiko, Antoine Martin","doi":"10.48327/mtsi.v3i1.2023.340","DOIUrl":null,"url":null,"abstract":"A 8-year-old schoolgirl from West Africa with no previous pathological history was admitted to the haematology department of the Brazzaville University Hospital for the management of cervical adenopathy. The diagnosis of sinus histiocytosis or Destombes-Rosaï-Dorfman disease was retained and the patient was treated with PO corticosteroids (methylprednisolone 32 mg/d then 16 mg/d). Given the rarity and uncertain aetiopathogeny of this syndrome, treatment is poorly codified. It includes corticosteroid therapy, immunomodulators and sometimes chemotherapy, radiotherapy or surgery, indicated in case of clinical manifestations of local organ compression. The disease may regress spontaneously. Its benignity does not justify systematic treatment in the absence of complications.","PeriodicalId":18493,"journal":{"name":"Medecine tropicale et sante internationale","volume":"3 1","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2023-03-14","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10300660/pdf/","citationCount":"0","resultStr":"{\"title\":\"[Cervical tumefaction in a child at Brazzaville University Hospital, Republic of the Congo].\",\"authors\":\"Alexis Elira Dokékias, Firmine Olivia Galiba Atipo Tsiba, Fortuné Bissiko, Antoine Martin\",\"doi\":\"10.48327/mtsi.v3i1.2023.340\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"A 8-year-old schoolgirl from West Africa with no previous pathological history was admitted to the haematology department of the Brazzaville University Hospital for the management of cervical adenopathy. The diagnosis of sinus histiocytosis or Destombes-Rosaï-Dorfman disease was retained and the patient was treated with PO corticosteroids (methylprednisolone 32 mg/d then 16 mg/d). Given the rarity and uncertain aetiopathogeny of this syndrome, treatment is poorly codified. It includes corticosteroid therapy, immunomodulators and sometimes chemotherapy, radiotherapy or surgery, indicated in case of clinical manifestations of local organ compression. The disease may regress spontaneously. Its benignity does not justify systematic treatment in the absence of complications.\",\"PeriodicalId\":18493,\"journal\":{\"name\":\"Medecine tropicale et sante internationale\",\"volume\":\"3 1\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2023-03-14\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10300660/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Medecine tropicale et sante internationale\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.48327/mtsi.v3i1.2023.340\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2023/3/31 0:00:00\",\"PubModel\":\"eCollection\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Medecine tropicale et sante internationale","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.48327/mtsi.v3i1.2023.340","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2023/3/31 0:00:00","PubModel":"eCollection","JCR":"","JCRName":"","Score":null,"Total":0}

引用次数: 0

摘要

布拉柴维尔大学医院（Brazzaville University Hospital）血液科收治了一名来自西非的 8 岁女学生，她以前没有病史。患者被诊断为窦组织细胞增生症或Destombes-Rosaï-Dorfman病，并接受了PO皮质类固醇治疗（甲基强的松龙32毫克/天，然后是16毫克/天）。由于这种综合征十分罕见，病因也不确定，因此治疗方法也不十分规范。治疗方法包括皮质类固醇治疗、免疫调节剂，有时还包括化疗、放疗或手术（在出现局部器官受压的临床表现时）。这种疾病可能会自发消退。在没有并发症的情况下，其良性程度并不证明有必要进行系统治疗。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

摘要图片

查看原文

微信好友朋友圈 QQ好友复制链接

本刊更多论文

[Cervical tumefaction in a child at Brazzaville University Hospital, Republic of the Congo].

A 8-year-old schoolgirl from West Africa with no previous pathological history was admitted to the haematology department of the Brazzaville University Hospital for the management of cervical adenopathy. The diagnosis of sinus histiocytosis or Destombes-Rosaï-Dorfman disease was retained and the patient was treated with PO corticosteroids (methylprednisolone 32 mg/d then 16 mg/d). Given the rarity and uncertain aetiopathogeny of this syndrome, treatment is poorly codified. It includes corticosteroid therapy, immunomodulators and sometimes chemotherapy, radiotherapy or surgery, indicated in case of clinical manifestations of local organ compression. The disease may regress spontaneously. Its benignity does not justify systematic treatment in the absence of complications.

求助全文

通过发布文献求助，成功后即可免费获取论文全文。去求助

来源期刊

Medecine tropicale et sante internationale

自引率

0.00%

发文量

期刊最新文献

[In the wake of Alphonse Laveran]. [Dr Jean Languillon (1912-2003), a major unrecognized leprologist]. [Stigmatization of people living with HIV in health care services in Togo]. [Analysis of national leprosy surveillance data in Mauritania from 2009 to 2019]. [Epidemiological characteristics of the Covid-19 epidemic between 2020 and 2022 in Kongo central, DRC].