Paediatric cystic fibrosis (CF)

End stage lung disease is characterized by a pro-inflammatory imbalance in the innate lymphoid cell compartment.

Pub Date : 2022-03-10 DOI: 10.1183/23120541.lsc-2022.180 O. Halle, M. Albrecht, S. Gaedcke, S. Pallenberg, Claudia Kessemeier, Sean Brüske, Lina Koch, Idalina M. Lüdemann, Emily Fuchshuber, Jan-Niklas Falke, Johanna Roediger, Marius Witt, Julia Camargo Neumann, Marina Schumacher, A. Chari Jirmo, G. Warnecke, D. Jonigk, P. Braubach, D. DeLuca, G. Hansen, A. Dittrich

Epithelial and neutrophil responses to microbes in cystic fibrosis airways

Pub Date : 2022-03-10 DOI: 10.1183/23120541.lsc-2022.179 D. Laucirica, C. Schofield, S. McLean, C. Margaroli, P. Agudelo-Romero, S. Stick, R. Tirouvanziam, T. Riley, A. Kicic, L. Garratt

Real-world effects of tezacaftor/ivacaftor (TEZ/IVA) in people with cystic fibrosis (pwCF): interim results of a long-term safety study using US CF Foundation Patient Registry (CFFPR) data

Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa2099 J. Bower, J. Shih, V. Seliger, D. Campbell, I. Berhane, R. Wu, A. Elbert