Pub Date : 2022-03-10DOI: 10.1183/23120541.lsc-2022.180
O. Halle, M. Albrecht, S. Gaedcke, S. Pallenberg, Claudia Kessemeier, Sean Brüske, Lina Koch, Idalina M. Lüdemann, Emily Fuchshuber, Jan-Niklas Falke, Johanna Roediger, Marius Witt, Julia Camargo Neumann, Marina Schumacher, A. Chari Jirmo, G. Warnecke, D. Jonigk, P. Braubach, D. DeLuca, G. Hansen, A. Dittrich
{"title":"End stage lung disease is characterized by a pro-inflammatory imbalance in the innate lymphoid cell compartment.","authors":"O. Halle, M. Albrecht, S. Gaedcke, S. Pallenberg, Claudia Kessemeier, Sean Brüske, Lina Koch, Idalina M. Lüdemann, Emily Fuchshuber, Jan-Niklas Falke, Johanna Roediger, Marius Witt, Julia Camargo Neumann, Marina Schumacher, A. Chari Jirmo, G. Warnecke, D. Jonigk, P. Braubach, D. DeLuca, G. Hansen, A. Dittrich","doi":"10.1183/23120541.lsc-2022.180","DOIUrl":"https://doi.org/10.1183/23120541.lsc-2022.180","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-03-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130404516","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2022-03-10DOI: 10.1183/23120541.lsc-2022.179
D. Laucirica, C. Schofield, S. McLean, C. Margaroli, P. Agudelo-Romero, S. Stick, R. Tirouvanziam, T. Riley, A. Kicic, L. Garratt
{"title":"Epithelial and neutrophil responses to microbes in cystic fibrosis airways","authors":"D. Laucirica, C. Schofield, S. McLean, C. Margaroli, P. Agudelo-Romero, S. Stick, R. Tirouvanziam, T. Riley, A. Kicic, L. Garratt","doi":"10.1183/23120541.lsc-2022.179","DOIUrl":"https://doi.org/10.1183/23120541.lsc-2022.179","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"13 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-03-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122970216","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa2099
J. Bower, J. Shih, V. Seliger, D. Campbell, I. Berhane, R. Wu, A. Elbert
{"title":"Real-world effects of tezacaftor/ivacaftor (TEZ/IVA) in people with cystic fibrosis (pwCF): interim results of a long-term safety study using US CF Foundation Patient Registry (CFFPR) data","authors":"J. Bower, J. Shih, V. Seliger, D. Campbell, I. Berhane, R. Wu, A. Elbert","doi":"10.1183/13993003.congress-2021.pa2099","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2099","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"59 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116846092","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3377
L. Balaneţchi, R. Selevestru, M. Cotorobai, D. Rotaru-Cojocari, Cristina Tomacinschi, N. Barbova, E. Gudumac, S. Şciuca
{"title":"Impact of Aspergillus fumigatus infection on lung function in children with cystic fibrosis","authors":"L. Balaneţchi, R. Selevestru, M. Cotorobai, D. Rotaru-Cojocari, Cristina Tomacinschi, N. Barbova, E. Gudumac, S. Şciuca","doi":"10.1183/13993003.congress-2021.pa3377","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3377","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"418 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"117334284","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3374
R. Bonhiver, N. Bricmont, Maud Pirotte, C. Moermans, M. Wuidart, J. Pirson, R. Louis, M. Seghaye, C. Kempeneers, H. Boboli
{"title":"Evidence for ciliary dyskinesia in cystic fibrosis","authors":"R. Bonhiver, N. Bricmont, Maud Pirotte, C. Moermans, M. Wuidart, J. Pirson, R. Louis, M. Seghaye, C. Kempeneers, H. Boboli","doi":"10.1183/13993003.congress-2021.pa3374","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3374","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129630253","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3378
Z. Sadeeva, I. Novikova, Natalya M. Alyabyeva, A. Lazareva, Y. Gorinova, O. Simonova
{"title":"Molecular genetic characteristics of Pseudomonas aeruginosa strains isolated from children with cystic fibrosis in Moscow","authors":"Z. Sadeeva, I. Novikova, Natalya M. Alyabyeva, A. Lazareva, Y. Gorinova, O. Simonova","doi":"10.1183/13993003.congress-2021.pa3378","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3378","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130767536","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3372
Beatrice Guidetti, A. Bos, E. C. van der Wiel, I. Meneghelli, M. M. van der Eerden, H. Tiddens, S. Volpi, H. Janssens
{"title":"Targeting Antibiotics to Pseudomonas aeruginosa in Small airways (TAPAS) in patients with Cystic Fibrosis","authors":"Beatrice Guidetti, A. Bos, E. C. van der Wiel, I. Meneghelli, M. M. van der Eerden, H. Tiddens, S. Volpi, H. Janssens","doi":"10.1183/13993003.congress-2021.pa3372","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3372","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"10 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116985704","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa2102
C. Castellani, N. Simmonds, C. Colombo, N. Kinnman, C. Desouza, T. Thorat, Marci L. Chew, K. Chandarana, K. van der Ent
{"title":"Respiratory microbiology outcomes from an observational study of ivacaftor in people with cystic fibrosis and non-G551D gating mutations (VOCAL)","authors":"C. Castellani, N. Simmonds, C. Colombo, N. Kinnman, C. Desouza, T. Thorat, Marci L. Chew, K. Chandarana, K. van der Ent","doi":"10.1183/13993003.congress-2021.pa2102","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2102","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"213 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126961761","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3366
M. Zampoli, R. Kassanjee, Janine Versraete, A. Westwood, H. Zar, B. Morrow
{"title":"Trends in cystic fibrosis (CF) survival in South Africa over 40 years","authors":"M. Zampoli, R. Kassanjee, Janine Versraete, A. Westwood, H. Zar, B. Morrow","doi":"10.1183/13993003.congress-2021.pa3366","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3366","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"15 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124503510","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.oa2677
M. Dumas, Nicholas Karsli, R. Jensen, F. Ratjen
{"title":"Evaluation of SnIII parameters as outcome measures of multiple breath washout (MBW) in preschool children with cystic fibrosis","authors":"M. Dumas, Nicholas Karsli, R. Jensen, F. Ratjen","doi":"10.1183/13993003.congress-2021.oa2677","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.oa2677","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"7 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123915478","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
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