A TYPICAL FEATURES IN IRVAN SYNDROME DEMONSTRATED ON MULTIMODAL IMAGING

Od Faao Hashim Ali Khan, Muhammad Aamir Shahzad, M. Awan
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Abstract

Purpose:Thepurposeofthis workwastodescribeidiopathicretinalvasculitis,aneurysms,andneuroretinitis(IRVAN)syndrome ina32-year-oldmale.Methods: Casereport.Case report: A 32-year-old male presented with acute visualdisturbance. Multimodal imaging revealed retinal vasculitis,aneurysmsandneuroretinitisinadditiontovitreousinflammation,retinalischemiaandepiretinalmembrane.Opticalcoherencetomographyangiography(OCTA)demonstratedmultiplemicroaneurysm inbotheyes.Conclusion: Multimodal imaging was helpful in diagnosinganddifferentiatingIRVANsyndromefromothersimilar-lookingclinicalentities.Retinalaneurysmsandretinalischaemiaweredetectablebyfundusfluoresceinangiography(FFA). However, OCTA showed multiple microaneurysmsthatwerenotclearlydifferentiablebyFFAbecauseofvitreousinflammationandvascularleakage.MicroaneurysmsinIRVAN syndrome area previously unreportedobservation.OCTAmayhelpdetectthesechangeswithaccuratedetails
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多模态影像显示了irvan综合征的典型特征
目的:本研究的目的是描述一名32岁男性的视网膜血管炎、动脉瘤和神经视网膜炎(IRVAN)综合征。方法:Casereport。病例报告:一名32岁男性,表现为急性视力障碍。多模态成像显示视网膜血管炎、动脉瘤、神经视网膜炎、玻璃体炎症、视网膜缺血和视网膜下膜,光学酒精血管造影(OCTA)显示双眼多发微动脉瘤。结论:眼底荧光血管造影(FFA)可检测视网膜动脉瘤和视网膜病变,多模态成像有助于诊断和鉴别视网膜病变。然而,OCTA显示多个微动脉瘤,由于玻璃体炎症和血管渗漏,无法通过ffa清晰区分。微动脉瘤在irvan综合征区域以前未见报道。OCTAmayhelpdetectthesechangeswithaccuratedetails
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UNUSUAL TREATMENT OPTION FOR PANUVEITIS ACUTE POSTERIOR MULTIFOCAL PLACOID PIGMENT EPITHELIOPATHY (APMPPE), ITSPOSSIBLE RELATIONSHIP WITH UROGENITAL TRACT DISORDER ANDTREATMENT ESOTROPIA WITH ECCENTRIC FIXATION LOCATION. CASE REPORT OF AN 11-YEAR FOLLOW-UP STUDY ON THE PATHOGENESIS OF DIABETIC RETINOPATHY, DAMAGE TO MULLER CELLS, DISEASES OF OPPONENTS, AND INFLAMMATION: A REVIEW A TYPICAL FEATURES IN IRVAN SYNDROME DEMONSTRATED ON MULTIMODAL IMAGING
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