Metopic Suture Synostosis ( Trigonocephaly ) : A Case Report

Abstract

Craniosynostosis is a premature fusion of single or multiple cranial sutures. It occurs in one of 2000–2500 live births (1, 2). Trigonocephaly is a form of craniosynostosis arising from the premature fusion and ossification of the metopic suture, which separates the two frontal bones and physiologically closes at 3–8 months of age (3, 4). Described first by Welcker in 1862, trigonocephaly is a Greek term meaning triangular forehead. Metopic synostosis occurs in between 1/700 and 1/15.000 newborns (5, 6). This results in a skull with a triangular forehead and deficient lateral orbital rims add to the supraorbital retrusion and bitemporal indentations. The growth restriction results in decreased intracranial volume. Thus, a surgical intervention is indicated to restore the volume of the skull along with appearance (7). This study aimed to present the case of a child born with trigonocephaly who was operated at 6 months of age with bifrontal craniotomy and fronto-orbital advancement.