{"title":"Rosai-Dorfman Disease of the Pineal Region: A Case Report","authors":"Yong-Hao Hou, Shubin Huang, Xiao-fan Ji","doi":"10.5580/2c8f","DOIUrl":null,"url":null,"abstract":"Rosai-Dorfman disease (RDD) is rare, especially in the central nervous system (CNS). We report a 4-year-old boy with a neoplasm in the pineal region, verified as RDD, with no concurrent clinical lymph node involvement. Emperipolesis was also identified in this case. Fibrosis was additionally found at extranodal sites. Positive results for the S100 protein and negative findings of CD1a were important for diagnosis.","PeriodicalId":232166,"journal":{"name":"The Internet Journal of Neurology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2012-08-08","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"The Internet Journal of Neurology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5580/2c8f","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0
Abstract
Rosai-Dorfman disease (RDD) is rare, especially in the central nervous system (CNS). We report a 4-year-old boy with a neoplasm in the pineal region, verified as RDD, with no concurrent clinical lymph node involvement. Emperipolesis was also identified in this case. Fibrosis was additionally found at extranodal sites. Positive results for the S100 protein and negative findings of CD1a were important for diagnosis.