Respiratory Monitoring in Pediatric Neuromuscular Disease

Andre Sugiyono, Siti Chandra Widjanantie
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Abstract

ABSTRACTDuring the outbreak of Covid-19, the policy of working from home for employees and studying from Neuromuscular disease in childhood result in dysfunction of chest wall and lung movement that interfere ventilation function and gas exchange. Without vital respiratory pump, ventilation, gas exchange function and cough ability would be compromised and could result in complications such as pneumonia, atelectasis, and respiratory failure. Comorbid factors in cardiovascular, musculoskeletal, nutrition, and gastrointestinal could aggravate respiratory morbidity and mortality if not adequately treated. This paper was written to review anatomy and physiology of neurorespiratory system, pathophysiology of respiratory complication in neuromuscular disease, clinical assessment and respiratory monitoring of childhood neuromuscular disease from Physical Medicine and Rehabilitation point of view.Keywords: assessment, neuromuscular disease, pediatric, respiratory
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小儿神经肌肉疾病的呼吸监测
【摘要】新冠肺炎疫情期间,员工在家办公和儿童神经肌肉疾病的学习政策导致胸壁和肺部运动功能障碍,干扰通气功能和气体交换。如果没有重要的呼吸泵,通气、气体交换功能和咳嗽能力将受到损害,并可能导致肺炎、肺不张和呼吸衰竭等并发症。如果治疗不当,心血管、肌肉骨骼、营养和胃肠道的合并症会加重呼吸道疾病的发病率和死亡率。本文从物理医学和康复学的角度,综述了神经呼吸系统的解剖生理学、神经肌肉疾病呼吸并发症的病理生理学、儿童神经肌肉疾病的临床评估和呼吸监测。关键词:评估,神经肌肉疾病,儿科,呼吸系统
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