Amy Cherry , Shriharsha Talluri , Richard Hessler , Benjamin Waldorf
{"title":"A rare case of renal leiomyosarcoma treated with partial nephrectomy","authors":"Amy Cherry , Shriharsha Talluri , Richard Hessler , Benjamin Waldorf","doi":"10.1016/j.eucr.2024.102835","DOIUrl":null,"url":null,"abstract":"<div><p>Renal Leiomyosarcoma (LMS) is an exceptionally rare and aggressive form of RCC (renal cell carcinoma), comprising of 0.5–1% of all adult RCC. This disease constitutes a 5-year 25 % overall survival. We present a rare case of renal leiomyosarcoma in a 58 year-old Caucasian female with final pathologic staging of pT2 who underwent robotic-assisted right partial nephrectomy. Despite negative margins, given her aggressive histology, adjunctive treatment is discussed.</p></div>","PeriodicalId":38188,"journal":{"name":"Urology Case Reports","volume":"56 ","pages":"Article 102835"},"PeriodicalIF":0.5000,"publicationDate":"2024-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S221444202400189X/pdfft?md5=739940a02d75aea3c6b84a46e797d00a&pid=1-s2.0-S221444202400189X-main.pdf","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Urology Case Reports","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S221444202400189X","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"UROLOGY & NEPHROLOGY","Score":null,"Total":0}
引用次数: 0
Abstract
Renal Leiomyosarcoma (LMS) is an exceptionally rare and aggressive form of RCC (renal cell carcinoma), comprising of 0.5–1% of all adult RCC. This disease constitutes a 5-year 25 % overall survival. We present a rare case of renal leiomyosarcoma in a 58 year-old Caucasian female with final pathologic staging of pT2 who underwent robotic-assisted right partial nephrectomy. Despite negative margins, given her aggressive histology, adjunctive treatment is discussed.