Yodit Abraham Yaynishet MD , Michael Teklehaimanot Abera MD , Kidist Amare Hagos MD , Woubedel Kiflu Aklilu MD , Nebyou Seyoum Abebe MD , Samuel Sisay Hailu MD
{"title":"Predominant visceral involvement and heterotopic ossification in Klippel-Trenaunay syndrome","authors":"Yodit Abraham Yaynishet MD , Michael Teklehaimanot Abera MD , Kidist Amare Hagos MD , Woubedel Kiflu Aklilu MD , Nebyou Seyoum Abebe MD , Samuel Sisay Hailu MD","doi":"10.1016/j.radcr.2024.12.053","DOIUrl":null,"url":null,"abstract":"<div><div>Klippel-Trenaunay Syndrome (KTS) is a complex vascular malformation disorder that primarily involves capillary, venous, and lymphatic anomalies, along with limb hypertrophy. This case report presents an atypical instance of KTS characterized by predominant visceral involvement and heterotopic ossification in a 6-year-old male patient. The child underwent surgical management with a favorable outcome.</div></div>","PeriodicalId":53472,"journal":{"name":"Radiology Case Reports","volume":"20 4","pages":"Pages 1834-1839"},"PeriodicalIF":0.0000,"publicationDate":"2025-01-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11783209/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Radiology Case Reports","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S1930043324014158","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"Medicine","Score":null,"Total":0}
引用次数: 0
Abstract
Klippel-Trenaunay Syndrome (KTS) is a complex vascular malformation disorder that primarily involves capillary, venous, and lymphatic anomalies, along with limb hypertrophy. This case report presents an atypical instance of KTS characterized by predominant visceral involvement and heterotopic ossification in a 6-year-old male patient. The child underwent surgical management with a favorable outcome.
期刊介绍:
The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.