[Congenital megalourethra].

Abstract

Megalourethra was described originally by Nesbitt as a rare congenital abnormally characterized by dilation of the peneal urethra. This defect has been classified as scaphoid or fusiform deformity. Because of its rarity we present this case diagnosed in the Neonatology Service of the Caja de Seguro Social of Panama. A male neonate with a 40 week gestation period arrived from the delivery room and we found a 5.5 cm long macropenia which had an 8 cm circumference and 2.5 cm width. It had a positive transillumination and was oozing urine. The ultrasonography showed dilation of the peneal urethra and two corpora cavernosa. Renal ultrasound showed bilateral hydronephrosis. The functional renogram with DTPA 99 Tc revealed normal bilateral renal function, dilated ureters which were redundant and proximal urethral obstruction. On cistourethrography, vesicoureteral bilateral reflux was observed, as well as stenosis of the proximal urethra. When he was a month old the infant underwent a vesicostomy and we decided to perform a urethroplasty when he is between 18 and 24 months old. Since the diagnosis was a type scaphoid megalourethra the prognosis is good. We hope that the postoperative results will enable our patient to have a normal sex life.