Extra-uterine low grade endometrioid stromal sarcoma arising from ovarian endometriosis: a case report and review of the literature.

Gynecologic oncology research and practice Pub Date : 2019-01-29 eCollection Date: 2019-01-01 DOI:10.1186/s40661-019-0067-7

Boubacar Efared, Ibrahim S Sidibé, Fatimazahra Erregad, Nawal Hammas, Laila Chbani, Hinde El Fatemi

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引用次数: 10

Abstract

Background: Endometrial stromal sarcoma (ESS) is a rare neoplasm accounting for only 0.2% of female genital tract tumors. The primary extra-uterine location of ESS is an extremely uncommon occurrence.

Case presentation: We present a case of a 64-year-old woman presenting with abdominopelvic and bilateral ovarian tumors with misleading clinical presentation and diagnostic challenge. The histopathological examination of the resected specimens disclosed the diagnosis of primary extra-uterine ESS arising from ovarian endometriosis. Adjuvant therapy with an aromatase inhibitor drug was prescribed for the patient, and she is still alive with no evidence of disease 7 months after surgery.

Conclusion: The awareness of the potential extra-uterine location of ESS should lead to correct diagnosis as this tumor has histopathological features and clinical behavior similar to its uterine counterpart.

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卵巢子宫内膜异位症引起的子宫外低级别子宫内膜样间质肉瘤1例报告及文献复习。

背景:子宫内膜间质肉瘤(ESS)是一种罕见的肿瘤，仅占女性生殖道肿瘤的0.2%。原发性ESS发生在子宫外是非常罕见的。病例介绍:我们提出了一个病例64岁的妇女表现为腹部盆腔和双侧卵巢肿瘤误导临床表现和诊断挑战。切除标本的组织病理学检查显示诊断为原发性子宫内膜异位症引起的子宫外ESS。为患者开了芳香酶抑制剂药物辅助治疗，手术后7个月，她仍然活着，无疾病迹象。结论:ESS具有与子宫肿瘤相似的组织病理特征和临床行为，对其潜在的子宫外位置的认识应有助于正确诊断。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Gynecologic oncology research and practice

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