[Ehlers-Danlos syndrome: Role of the dentist].

Abstract

The Ehlers-Danlos syndrome (EDS) is a group of genetic connective tissue disorder due to abnormal collagen synthesis. EDS is characterized by the triad: joint hypermobility - skin hyperextensibility - connective tissue friability leading to vascular and skin fragility. Thirteen forms exist including three main ones: the hypermobile, classical and vascular forms. Given the diversity of clinical manifestations, the diagnosis of EDS is difficult. The management of this syndrome is multidisciplinary and includes the dental surgeon, because EDS can have many oral and dental manifestations. This syndrome can lead to dental, periodontal, mucosal damage and also to joint damage to the manducatory apparatus. The authors, after describing the symptoms of EDS, their manifestations and their detection, will explain the implications in odontostomatology. EDS must be known to the dentist because it can lead to precautions during dental care, and because patients with EDS are more prone to temporomandibular disorders. At the last, the many oral and dental manifestations of EDS give the dentist an important role in screening for this syndrome.