Isabella Hana Bertuol Kinoshita , Ulysses S. Torres , Lilian Aguiar Pupo Zanini , Maria Fernanda Pinto , Julia de Castro Vieira Veloso , Glaucio Rodrigo Silva de Siqueira , Giuseppe D'Ippolito
{"title":"The Ductal Plate From the Inside Out: An Illustrated Review of Fibropolycystic Liver Disease","authors":"Isabella Hana Bertuol Kinoshita , Ulysses S. Torres , Lilian Aguiar Pupo Zanini , Maria Fernanda Pinto , Julia de Castro Vieira Veloso , Glaucio Rodrigo Silva de Siqueira , Giuseppe D'Ippolito","doi":"10.1053/j.sult.2022.06.008","DOIUrl":null,"url":null,"abstract":"<div><p><span><span>Fibropolycystic liver disease is a continuum of disorders that result from insults to the ductal plate at different stages of development and are often associated with each other. Caroli's syndrome, </span>polycystic liver disease<span>, biliary hamartomas<span><span><span>, and congenital hepatic fibrosis<span> are included in this complex spectrum that also shows frequent association with renal anomalies, such as </span></span>polycystic kidney disease and </span>medullary sponge kidney. </span></span></span>Choledochal cysts are a controversial point in this topic since they have long been considered part of this spectrum due to morphological similarities, but studies have shown different pathogenesis. This article's purpose is to review these abnormalities through a multimodality radiological perspective offering correlation with its key embryological aspects. Knowing these numerous anomalies and their possible associations may ease an accurate diagnosis and prompt management.</p></div>","PeriodicalId":49541,"journal":{"name":"Seminars in Ultrasound Ct and Mri","volume":null,"pages":null},"PeriodicalIF":1.5000,"publicationDate":"2022-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Seminars in Ultrasound Ct and Mri","FirstCategoryId":"3","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S088721712200066X","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING","Score":null,"Total":0}
引用次数: 1
Abstract
Fibropolycystic liver disease is a continuum of disorders that result from insults to the ductal plate at different stages of development and are often associated with each other. Caroli's syndrome, polycystic liver disease, biliary hamartomas, and congenital hepatic fibrosis are included in this complex spectrum that also shows frequent association with renal anomalies, such as polycystic kidney disease and medullary sponge kidney. Choledochal cysts are a controversial point in this topic since they have long been considered part of this spectrum due to morphological similarities, but studies have shown different pathogenesis. This article's purpose is to review these abnormalities through a multimodality radiological perspective offering correlation with its key embryological aspects. Knowing these numerous anomalies and their possible associations may ease an accurate diagnosis and prompt management.
期刊介绍:
Seminars in Ultrasound, CT and MRI is directed to all physicians involved in the performance and interpretation of ultrasound, computed tomography, and magnetic resonance imaging procedures. It is a timely source for the publication of new concepts and research findings directly applicable to day-to-day clinical practice. The articles describe the performance of various procedures together with the authors'' approach to problems of interpretation.