A rare Case of Rhabdomyosarcoma presenting as Gradenigo syndrome in a child

Abstract

Objective: To study a rare case of Rhabdomyosarcoma. Methods: Observational descriptive study of a case, a 3-year-old female child, presenting to our OPD. She was thoroughly examined and radiological investigations (HRCT Temporal bone and MRI Brain) were done. The Neurosurgery department proceeded with a biopsy of the lesion by left temporal bone craniotomy through subtemporal approach. Results: Histopathology suggested a Rhabdomyosarcoma of anaplastic type. The patient then underwent 6 cycles of Chemoradiation. Conclusion: The awareness that Rhabdomyosarcoma of petrous apex can present as Gradenigo syndrome along with 7th nerve palsy is important for the early diagnosis and its treatment.