Neurological manifestations of Degos disease

Abstract

Degos disease is a rare disease that manifests itself as multifocal vasculopathy, the consequence of which is the defeat of many systems, including the nervous system. This disease is difficult to diagnose, today it does not have a standardized approach to treatment, and it is deadly.In the presented clinical case, the course of BD is described in a 66-year-old patient, whose debut of the disease was a lesion of the skin. The cause of hospitalization of the patient was the defeat of the central nervous system. During the additional examination, the patient was diagnosed with ischemic stroke in the basin of the left middle cerebral artery, posterior cerebral artery, right middle cerebral artery of another established etiology according to TOAST, aseptic leptomeningitis, pachymeningitis. The course of the disease was complicated by damage to the gastrointestinal tract, the cardiovascular system, as well as the addition of a coronavirus infection, which led to death.