Case of Laryngeal Atresia, Tracheal Agenesis, Tracheo-Esophageal Fistula, Double Outlet Right Ventricle and Persistent Left Superior Vena Cava

Abstract

Congenital high airway obstruction syndrome (CHAOS) includes laryngeal atresia and tracheal agenesis which are rare and potentially lethal conditions. We describe a newborn term infant with laryngeal atresia and tracheal agenesis with a distal tracheo-esophageal fistula (TEF). He also had a double outlet right ventricle (DORV) and a persistent left superior vena cava (LSVC). To our knowledge this is the first report of this association.