Sinonasal biphenotypic sarcoma of uvula: the first case report

Abstract

Biphenotypic sinonasal sarcoma is a rare entity and it is a new term included in literature recently. It affects sinonasal tract exclusively but we report the first case of biphenotypic sinonasal sarcoma of uvula. The patient is a 56-year-old male who had a mass in the oropharynx hanging from the uvula exclusively. Contrast enhanced computed tomography of oral cavity reported homogenously enhancing benign mass arising from uvula probably pleomorphic adenoma. It was excised in toto and sent for histopathological examination. The detailed histopathological analysis concluded the diagnosis as sinonasal biphenotypic sarcoma of uvula. Sinonasal biphenotypic sarcoma is exclusively found in sinonasal tract. Occurrence of this entity in uvula is first of its kind and needs special attention.