Amelogenesis Imperfecta: Longevity of Clinical Treatment in Pediatric Dentistry

Abstract

Amelogenesis Imperfecta (AI) is a rare, hereditary disorder that causes a defect in enamel mineralization in the primary and permanent dentitions. Amelogenesis imperfecta is generally categorized as hypoplastic, hypocalcified, or hypomaturation form based on the primary enamel defect. However, distinctive clinical features may be seen in each variant. Moreover, compromised esthetic appearances, tooth sensitivity and loss of occlusal vertical dimension are the common clinical problems observed in these variants. The objective of this review was to discuss the management strategies for patients with amelogenesis imperfecta. Definite diagnosis and adequate treatment planning are ensured for patients clinically presented with different forms of AI. Clinicians should provide preventive care and establish an early permanent therapy plan for these patients. Nevertheless, an interdisciplinary approach is required to improve both esthetic and functions. Moreover, there is a need for long-lasting restorative solutions for AI patients.